Viktor Hraška · Peter Murín Surgical Management of Congenital Heart Disease II Single Ventricle and Hypoplastic Left Heart Syndrome Aortic Arch Anomalies Septal Defects and Anomalies in Pulmonary Venous Return Anomalies of Thoracic Arteries and Veins A Video Manual DVDROM 123 INCLUDED Surgical Management of Congenital Heart Disease II Viktor Hraška · Peter Murín Surgical Management of Congenital Heart Disease II Single Ventricle and Hypoplastic Left Heart Syndrome Aortic Arch Anomalies Septal Defects and Anomalies in Pulmonary Venous Return Anomalies of Thoracic Arteries and Veins A Video Manual 1 3 Viktor Hraška, MD Ph.D. Peter Murín, MD German Pediatric Heart German Pediatric Heart Centre, Sankt Augustin Centre, Sankt Augustin Department of Cardiac Surgery Department of Cardiac Surgery Arnold Janssen Straße 29 Arnold Janssen Straße 29 53757 Sankt Augustin 53757 Sankt Augustin Germany Germany [email protected] [email protected] ISBN 978-3-662-44069-8 ISBN 978-3-662-44070-4 (eBook) DOI 10.1007/978-3-662-44070-4 Library of Congress Control Number: 2012932861 Springer Heidelberg Dordrecht London New York © Springer-Verlag Berlin Heidelberg 2015 This work is subject to copyright. All rights are reserved by the Publisher, whether the whole or part of the mate- rial is concerned, specifically the rights of translation, reprinting, reuse of illustrations, recitation, broadcasting, reproduction on microfilms or in any other physical way, and transmission or information storage and retrieval, electronic adaptation, computer software, or by similar or dissimilar methodology now known or hereafter devel- oped. Exempted from this legal reservation are brief excerpts in connection with reviews or scholarly analysis or material supplied specifically for the purpose of being entered and executed on a computer system, for exclusive use by the purchaser of the work. Duplication of this publication or parts thereof is permitted only under the provi- sions of the Copyright Law of the Publisher´s location, in its current version, and permission for use must always be obtained from Springer. Permissions for use may be obtained through RightsLink at the Copyright Clearance Center. Violations are liable to prosecution under the respective Copyright Law. The use of general descriptive names, registered names, trademarks, service marks, etc. in this publication does not imply, even in the absence of a specific statement, that such names are exempt from the relevant protective laws and regulations and therefore free for general use. Product liability: The publishers can not guarantee the accuracy of any information about dosage and application contained in this book. In every individual case the user must check such information by consulting the relevant literature. Printed on acid-free paper Springer is part of Springer Science+Business Media www.springer.com Dedicated to the medical personnel at the Deutsches Kinderherzzentrum, Sankt Augustin, Germany Preface Encouraged by the success of the first volume of the multimedia cardiac sur- gical video manual, we have put a lot of effort into completing the second volume, which includes the remaining operations carried out in patients with congenital heart disease that were not dealt with in the previous volume. The proven format of the first volume has been preserved. Each individual chapter first addresses a specific surgical anatomy and indication for surgery; this is followed by narrated video clips depicting the operative approach and tech- nique. Recently, some aspects of perfusion and operative management have been modified and refined. Therefore, some chapters, such as “Hypoplastic left heart syndrome”, show the progress in different strategies of perfusion and surgical management, with the aim of mirroring my current surgical practice. I believe that the second volume will again be of benefit to all clinicians, rang- ing from medical students and nurses to cardiologists and cardiac surgeons, in other words, all those responsible for the care of children with congenital heart diseases. It may also assist cardiac surgeons when dealing with rare defects, such as pulmonary artery sling, biventricular management of hypoplastic left heart complex, the Nikaidoh operation for the transposition of the great arteries with pulmonary stenosis, and complete atrioventricular septal defect etc. Viktor Hraška Sankt Augustin, Germany, 2014 VII VIII V. Hraška, P. Murín Acknowledgements I am grateful to my coauthor, Peter Murín MD, for his assistance in all op- erations and for editing the video clips. I am indebted to Christian Walter for his technical support in processing the edited video clips. I wish to thank to Prof. Boulos Asfour MD, not only for his support, but for his contribution to the chapter “Atrial septal defect”, in which he elaborates his technique of mini-invasive closure of an atrial septal defect. I would like to thank Elizabeth Grundy for her help in preparing the manuscript. I thank our team of cardiac surgeons, cardiologists, anaesthetists, intensivists, perfusionists, pediatricians, scrub nurses and nurses who take care of our patients at the Deutsches Kinder- herzzentrum Sankt Augustin. The last, but not least I thank Stiftung Deutsches Kinderherzzentrum Sankt Augustin for sponsoring this project. Viktor Hraška Sankt Augustin, Germany, 2014 Contents 1 Single Ventricle 1 ◙ Introduction 2 ◙ Anatomy 3 ◙ Single Ventricle with DILV 3 ◙ Single Ventricle with DIRV 4 ◙ Single Ventricle with Mitral Atresia 5 ◙ Single Ventricle with Tricuspid Atresia 5 ◙ Single Ventricle with Unbalanced AV Canal Defect 6 ◙ Single Ventricle with Heterotaxy Syndrome 6 ◙ Other Single Ventricle 6 ◙ Indication for Surgery 7 ◙ Stage I Palliation – Initial Palliative Procedures (Neonates & Infants < 4 Months Old) 7 ◙ Stage II Palliation – Superior Cavopulmonary Anastomosis (Infants 4–6 Months of Age) 8 ◙ Stage III Palliation – The Total Cavopulmonary Connection (Children >18 Months Age) 9 ◙ Approach and Cardiopulmonary Bypass Strategy 10 ◙ Initial Palliative Procedures without Cardiopulmonary Bypass 10 ◙ Initial Palliative Procedures with Cardiopulmonary Bypass 10 ◙ Physiologically Corrective Procedures 10 ◙ Bidirectional Cavopulmonary Anastomosis without Cannulation of the Superior Vena Cava 11 ◙ Patient Characteristics 11 ◙ Specific Steps of Surgery 11 ◙ Bidirectional Cavopulmonary Anastomosis with Cannulation of the Superior Vena Cava 16 ◙ Patient Characteristics 16 ◙ Specific Steps of Surgery 16 ◙ Extracardiac Conduit with Fenestration 20 ◙ Patient Characteristics 20 ◙ Specific Steps of Surgery 21 ◙ Extracardiac Conduit Connecting the Hepatic Veins with the Left Pulmonary Artery in a Patient with Situs Inversus 26 ◙ Patient Characteristics 26 ◙ Specific Steps of Surgery 27 IX X V. Hraška, P. Murín ◙ Decompression of the Thoracic Duct by Diverting the Innominate Vein into the Right Atrium in a High-Risk Fontan Patient 32 ◙ Patient Characteristics 32 ◙ Specific Steps of Surgery 33 ◙ Recommended References 36 2 Hypoplastic Left Heart Syndrome 39 ◙ Introduction 40 ◙ Anatomy 41 ◙ Indication for Surgery 42 ◙ Initial Procedures (Neonates) 42 ◙ Approach and Cardiopulmonary Bypass Strategy 43 ◙ Hybrid Procedure 43 ◙ Norwood Stage I Palliation 43 ◙ Norwood Stage I. Palliation with Double Aortic Cannulation and Whole Body Perfusion 44 ◙ Patient Characteristics 44 ◙ Specific Steps of Surgery 45 ◙ Double Barrel Damus-Kaye-Stansel Anastomosis with Reconstruction of the Aortic Arch and Modified Blalock-Taussig Shunt 50 ◙ Patient Characteristics 50 ◙ Specific Steps of Surgery 51 ◙ Norwood Stage I. Palliation After Bilateral Pulmonary Artery Banding – Staged Approach 58 ◙ Patient Characteristics 58 ◙ Specific Steps of Surgery 59 ◙ Biventricular Repair – The First Stage: Norwood Stage I. Palliation with Sano Shunt and Enlargement of the Ventricular Septal Defect 66 ◙ Patient Characteristics 66 ◙ Specific Steps of Surgery 66 ◙ Biventricular Repair – The Second Stage: Intraventricular Rerouting of the Left Ventricle to the Systemic Outflow and the Right Ventricle to the Pulmonary Artery Conduit 72 ◙ Patient Characteristics 72 ◙ Specific Steps of Surgery 73 ◙ Recommended References 78 3 Coarctation of the Aorta 81 ◙ Introduction 82 ◙ Anatomy 83 ◙ Indication for Surgery 84 Contents XI ◙ Neonates 84 ◙ Infants 86 ◙ Childhood and Adolescence 86 ◙ Re-Coarctation 86 ◙ Management Consideration – Controversy 87 ◙ Approach and Cardiopulmonary Bypass Strategy 88 ◙ Resection of Aortic Coarctation and Extended End-to-End Anastomosis 90 ◙ Patient Characteristics 90 ◙ Specific Steps of Surgery 90 ◙ Resection of Aortic Coarctation and End-to-Side Anastomosis Through a Median Sternotomy 95 ◙ Patient Characteristics 95 ◙ Specific Steps of Surgery 95 ◙ Resection of a Stented Isthmus of the Aorta and Reconstruction of the Aortic Arch with Partial End-to-End Anastomosis and Pericardial Patch Plasty 100 ◙ Patient Characteristics 100 ◙ Specific Steps of Surgery 101 ◙ Resection of a Stented Isthmus of the Aorta and Reconstruction of the Aortic Arch by Pericardial Patch Plasty 105 ◙ Patient Characteristics 105 ◙ Specific Steps of Surgery 106 ◙ Reimplantation of the Right Aberrant Subclavian Artery into the Right Carotid Artery; Resection of the Stented Coarctation and End-to-End Anastomosis; Patch Closure of the Ventricular Septal Defect 108 ◙ Patient Characteristics 108 ◙ Specific Steps of Surgery 109 ◙ Extra-Anatomical Jump Graft Between the Ascending and Descending Aorta, Using a 18 mm Ø Prosthesis 112 ◙ Patient Characteristics 112 ◙ Specific Steps of Surgery 113 ◙ Recommended References 116 4 Interruption of the Aortic Arch 119 ◙ Introduction 120 ◙ Anatomy 120 ◙ Indication for Surgery 121 ◙ Approach and Cardiopulmonary Bypass Strategy 122 ◙ Aortic Arch Reconstruction by Subclavian Flap and Pericardial Patch Plasty in a Patient with an Interrupted Aortic Arch Type B 123 ◙ Patient Characteristics 123 ◙ Specific Steps of Surgery 124