Extraordinary Disorders of Human Behavior CRITICAL ISSUES IN PSYCHIATRY An Educational Series for Residents and Clinicians Series Editor: Sherwyn M. Woods, MD., PhD. Universiryl of SOli them Cnlifomin School of Medicine Los Angeles, Cnlifomin A RESIDENT'S GUIDE TO PSYCHIATRIC EDUCATION Edited by Michael G. G. Thompson, MD. STATES OF MIND: Analysis of Change in Psychotherapy Mardi J. Horowitz, MD. DRUG AND ALCOHOL ABUSE: A Clinical Guide to Diagnosis and Treatment Marc A. Schuckit, MD. THE INTERFACE BETWEEN THE PSYCHODYNAMIC AND BEHAVIORAL THERAPIES Edited by Judd Marmor, MD., and Sherwyn M. Woods, MD., Ph.D. LAW IN THE PRACTICE OF PSYCHIATRY Seymour L. Halleck, MD. NEUROPSYCHIATRIC FEATURES OF MEDICAL DISORDERS James W. Jefferson, MD., and John R. Marshall, MD. ADULT DEVELOPMENT: A New Dimension in Psychodynamic Theory and Pradice Calvin A. Colarusso, M.D., and Robert A. Nemiroff, M.D. SCHIZOPHRENIA John S. Strauss, MD., and William T. Carpenter, Jr., MD. EXTRAORDINARY DISORDERS OF HUMAN BEHAVIOR Edited by Claude T. H. Friedmann, MD., and Robert A. Faguet, MD. MARITAL THERAPY: A Combined Psychodynamic-Behavioral Approach Edited by R. Taylor Segraves, MD. TREATMENT INTERVENTIONS IN HUMAN SEXUALITY Edited by Carol C. Nadelson, MD., and David B. Marcotte, MD. A Continuation Order Plan is available for this series. A continuation order will bring delivery of each new volume immediately upon publication. Volumes are billed only upon actual shipment. For further information please contact the publisher. Extraordinary Disorders of Human Behavior Edited by CLAUDE T. H. FRIEDMANN, M. D. University of California at Irvine Medical Center Orange, California and ROBERT A. FAGUET, M. D. Universihj of California III Los Angeles School of Medicine Los Angeles, Califonzia PLENUM PRESS . NEW YORK AND LONDON Library of Congress Cataloging in Publication Data Main entry under title: Extraordinary disorders of human behavior. (Critical issues in psychiatry) Bibliography: p. Includes index. 1. Psychology, Pathological-Addresses, essays, lectures. I. Friedmann, Claude T. H. II. Faguet, Robert Andrew. III. Series. [DNLM: 1. Mental disorders. WM 100 E965j RC454.4.E925 1982 616.89 82-12286 ISBN-13: 978-1-4615-9253-2 e-ISBN-13: 978-1-4615-9251-8 DOl: 10.1 007/978-1-4615-9251-8 © 1982 Plenum Press, New York Softcover reprint of the hardcover 1s t edition 1982 A Division of Plenum Publishing Corporation 233 Spring Street, New York, N.Y. 10013 All rights reserved No part of this book may be reproduced, stored in a retrieval system, or transmitted in any form or by any means, electronic, mechanical, photocopying, microfilming, recording, or otherwise, without written permission from the publisher Contributors FARUK S. ABUZZAHAB, SR., M.D., Ph.D. • Associate Clinical Professor of Psychiatry, University of Minnesota, 606 South 24th Avenue, #818, Minneapolis MN 55454 RANSOM J. ARTHUR, M.D .• Dean, School of Medicine, The Oregon Health Sciences University 3181 S.W. Sam Jackson Park Road, Portland, OR 97201 DANIEL B. AUERBACH, M.D .• Adjunct Assistant Professor of Psychiatry, University of California at Los Angeles, 15760 Ventura Boulevard, #1929, Encino CA 91436 BURTON G. BURTON-BRADLEY, M.D .• Honorary Professor of Psychiatry, University of New Zealand; Mental Health Services, P.O. Box 1239, Boroko, Papua New Guinea HARRY D. EASTWELL, M.D .• Senior Lecturer in Psychiatry, Royal Brisbane Hospital, Brisbane, Queensland 4029, Australia KAY F. FAGUET, Ph.D. • Assistant Clinical Professor of Psychiatry (Psychology), University of California at Los Angeles, Neuropsychiatric Institute, 760 Westwood Plaza, Los Angeles CA 90024 ROBERT A. FAGUET, M.D .• Assistant Clinical Professor of Psychiatry, University of California at Los Angeles, 11665 W. Olympic Boulevard, Suite 410, Los Angeles, CA 90064 CHARLES V. FORD, M.D .• Professor of Psychiatry, Vanderbilt University School of Medicine, Nashville TN 37232 CLAUDE T. H. FRIEDMANN, M.D .• Assistant Professor of Psychiatry, University of California at Irvine, 101 City Drive South, Orange, CA 92668 v vi CONTRIBUTORS JAMES S. GROTSTEIN, M.D .• Clinical Professor of Psychiatry, University of California at Los Angeles, 9777 Wilshire Boulevard, Los Angeles CA 90212 KAY REDFIELD JAMISON, Ph.D. • Assistant Professor of Psychiatry (Psychology) and Director, University of California at Los Angeles, Affective Disorders Clinic, Los Angeles CA 90024 IRA M. LESSER, M.D .• Assistant Professor of Psychiatry, University of California at Los Angeles, Harbor General-UCLA Medical Center, Building D-5, Psychiatry, 1000 West Carson Street, Torrance CA 90509 E. MANSELL PATTISON, M.D .• Chairman and Professor, Department of Psychiatry and Health Behavior, Medical College of Georgia, Augusta, GA 30901 ROBERT F. REBAL, JR., M.D .• Assistant Professor of Psychiatry, University of Southern California School of Medicine, 1934 Hospital Place, Los Angeles CA 90033 ROBERT T. RUBIN, M.D., Ph.D. • Professor of Psychiatry, University of California at Los Angeles, Harbor General-UCLA Medical Center, Building B-4, 1000 West Carson Street, Torrance CA 90509 DAVID RUDNICK, M.D., Ph.D. • Assistant Clinical Professor of Psychiatry, University of California at Los Angeles- Neuropsychiatric Institute, 19144-9 Hamlin Street, Reseda CA 91335 JOSEPH WESTERMEYER, M.D., Ph.D. • Professor of Psychiatry, University of Minnesota, Department of Psychiatry, University Hospitals, Box 393, Mayo Memorial Building, Minneapolis, MN 55455 SHERWYN WOODS, M.D., Ph.D. • Professor of Psychiatry, University of Southern California, 1934 Hospital Place, Los Angeles CA 90033 Foreword Clinicians have long been fascinated by the rare and exotic in med- icine. Similarly, psychiatrists and mental health professionals have been intrigued by the uncommon and extraordinary syndromes which, despite their rarity, have much to teach us about the limitless forms of human adaptation. Of particular interest is the fact that fragments and partial expressions of these rare disorders are often encountered in the dreams and fantasies of the "ordinary" patient. For this reason, the understanding and insights collected in this volume are likely to have clinical usefulness far beyond those rare occasions when we encounter the exotic in its fully developed form. These disorders demonstrate the complex interplay between intra- psychic dynamic forces and the cultural influences which act to shape overt symptomatology. The section on extraordinary syndromes from non-Western cultures demonstrates the universality of the psychody- namic roots of human suffering, despite the seemingly strange furms in which this suffering is expressed. As clinicians we are too often restricted by ethnocentric attitudes and culturally determined stereotypes. This volume provides a stimulating and enjoyable opportunity to reach beyond those limitations. Sherwyn M. Woods Series Editor vii Preface Human personality, the most complex organization known, has evolved a staggering variety of adaptive mechanisms. Its plasticity is described by Kolb (1977): Since adaptation is the very essence of life, it is not strange that man, the most highly developed species, has evolved not only anatomical adjust- ments, which protect him structurally or physiologically in respect to his environment, but also psychological devices, which assist him in dealing with emotional needs and stresses. These devices help meet the needs for affection, personal security, personal significance, and defense against per- turbing affects. (p. 11) There are a number of disorders, however, that represent atypical adaptations in that they do not easily conform to standard diagnostic frameworks (neither in Kraepelin's time nor in the modern era of DSM- III). These entities have usually been termed uncommon, rare, exotic, esoteric, extraordinary, and unclassifiable. These "fragments," as Lehmann (1975) calls them, are scattered widely over the literature. We have attempted to contemporize and update them in one clinically relevant volume. It is our impression that even though the general psychiatrist may encounter only one or two such disorders in his lifetime, he will most certainly see their innumer- able partial and fragmentary expressions in his patients' dreams, fanta- sies, and behaviors. An interest in, and familiarity with, these syndromes will therefore assist him, we hope, in understanding and treating his patients. We hope, too, that new interest will be stimulated in these disorders; not only do we find them individually fascinating but we recognize that the study of unusual syndromes often helps elucidate the more common disorders. Finally, in accordance with the current trend in American psychia- try to revise diagnostic criteria and improve the reliability of diagnostic judgments (Spitzer, 1978), we wonder: Will these syndromes continue to stand apart as ungrouped entities or will they be seen in the future as "typical" variants of the more common psychiatric disorders? In addition to the sections on rare syndromes and extraordinary pre- ix x PREFACE sentations of common syndromes, we are including a section on extraor- dinary syndromes from non-Western cultures. These entities are further illustrations of the extraordinary evolution of psychological self-preser- vation and underscore the notion that what is extraordinary in one cul- ture may not be so in another. Human behavior is in part culturally determined and must always be judged in context. C.T.H.F. R.A.F. REFERENCES Kolb, 1. c., 1977, "Modern Clinical Psychiatry," W. B. Saunders, Philadelphia. Lehmann, H. E., 1975, Unusual psychiatric disorders and atypical psychoses, in "Compre- hensive Textbook of Psychiatry II" (A. Freedman, H. Kaplan, and B. Sadock, eds.), pp. 1724-1736, Williams and Wilkins, Baltimore. Spitzer, R. 1., 1978, Foreword, in "DSM-II1: Diagnostic Criteria Draft," Task Force on Nomenclature and Statistics, American Psychiatric Association. Contents 1 La Folie a Deux . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 1 Robert A. Faguet and Kay F. Faguet Case Examples. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 3 Epidemiology ..................................... 6 Subtypes of Folie a Deux ........................... 8 Etiology. . . . . . . . . . . . . . . ... . . . . . . . . . . . . . . . . . . . . . . . . . 8 Differential Diagnosis. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 11 Treatment. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 12 References . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 13 2 Munchausen Syndrome. . . . . . . . . . . . . . . . . . . . . . . 15 Charles V. Ford Introduction. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 15 Historical Origins of the Munchausen Stories . . . . . . . . . 15 Case Reports. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 16 Phenomenology of the Syndrome ................... 17 Etiologic Hypotheses of the Syndrome. . . . . . . . . . . . . . . 20 Treatment and Management . . . . . . . . . . . . . . . . . . . . . . . . 23 Conclusions and Summary. . . . . . . . . . . . . . . . . . . . . . . . . . 25 References . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 25 3 The Ganser Syndrome 29 Daniel B. Auerbach The Symptom of Approximate Answers. . . . . . . . . . . . . . 31 What is the True Syndrome? A Review of Cases in the Literature . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 32 xi